- BBS4 is a minor contributor to Bardet-Biedl syndrome and may also participate in triallelic inheritance. Katsanis, N., Eichers, E.R., Ansley, S.J., Lewis, R.A., Kayserili, H., Hoskins, B.E., Scambler, P.J., Beales, P.L., Lupski, J.R. Am. J. Hum. Genet. (2002)