- A cysteine substitution in the zona pellucida domain of alpha-tectorin results in autosomal dominant, postlingual, progressive, mid frequency hearing loss in a Spanish family. Moreno-Pelayo, M.A., del Castillo, I., Villamar, M., Romero, L., Hernández-Calvín, F.J., Herraiz, C., Barberá, R., Navas, C., Moreno, F. J. Med. Genet. (2001)