- X-linked late-onset sensorineural deafness caused by a deletion involving OA1 and a novel gene containing WD-40 repeats. Bassi, M.T., Ramesar, R.S., Caciotti, B., Winship, I.M., De Grandi, A., Riboni, M., Townes, P.L., Beighton, P., Ballabio, A., Borsani, G. Am. J. Hum. Genet. (1999)