- Loss of K-Cl co-transporter KCC3 causes deafness, neurodegeneration and reduced seizure threshold. Boettger, T., Rust, M.B., Maier, H., Seidenbecher, T., Schweizer, M., Keating, D.J., Faulhaber, J., Ehmke, H., Pfeffer, C., Scheel, O., Lemcke, B., Horst, J., Leuwer, R., Pape, H.C., Völkl, H., Hübner, C.A., Jentsch, T.J. EMBO J. (2003)