Gene Review:
SYVN1 - synovial apoptosis inhibitor 1, synoviolin
Homo sapiens
Synonyms:
DER3, E3 ubiquitin-protein ligase synoviolin, HRD1, KIAA1810, Synovial apoptosis inhibitor 1
- Molecular characterization and chromosomal localization of a third alpha-class hypoxia inducible factor subunit, HIF3alpha. Gu, Y.Z., Moran, S.M., Hogenesch, J.B., Wartman, L., Bradfield, C.A. Gene Expr. (1998)
- Synoviolin/Hrd1, an E3 ubiquitin ligase, as a novel pathogenic factor for arthropathy. Amano, T., Yamasaki, S., Yagishita, N., Tsuchimochi, K., Shin, H., Kawahara, K., Aratani, S., Fujita, H., Zhang, L., Ikeda, R., Fujii, R., Miura, N., Komiya, S., Nishioka, K., Maruyama, I., Fukamizu, A., Nakajima, T. Genes Dev. (2003)
- A complex of Yos9p and the HRD ligase integrates endoplasmic reticulum quality control into the degradation machinery. Gauss, R., Jarosch, E., Sommer, T., Hirsch, C. Nat. Cell Biol. (2006)
- Cytoplasmic destruction of p53 by the endoplasmic reticulum-resident ubiquitin ligase 'Synoviolin'. Yamasaki, S., Yagishita, N., Sasaki, T., Nakazawa, M., Kato, Y., Yamadera, T., Bae, E., Toriyama, S., Ikeda, R., Zhang, L., Fujitani, K., Yoo, E., Tsuchimochi, K., Ohta, T., Araya, N., Fujita, H., Aratani, S., Eguchi, K., Komiya, S., Maruyama, I., Higashi, N., Sato, M., Senoo, H., Ochi, T., Yokoyama, S., Amano, T., Kim, J., Gay, S., Fukamizu, A., Nishioka, K., Tanaka, K., Nakajima, T. EMBO J. (2007)
- Determinants of RING-E2 Fidelity for Hrd1p, a Membrane-anchored Ubiquitin Ligase. Bazirgan, O.A., Garza, R.M., Hampton, R.Y. J. Biol. Chem. (2006)
- A ubiquitin ligase HRD1 promotes the degradation of Pael receptor, a substrate of Parkin. Omura, T., Kaneko, M., Okuma, Y., Orba, Y., Nagashima, K., Takahashi, R., Fujitani, N., Matsumura, S., Hata, A., Kubota, K., Murahashi, K., Uehara, T., Nomura, Y. J. Neurochem. (2006)
- High ER stress in beta-cells stimulates intracellular degradation of misfolded insulin. Allen, J.R., Nguyen, L.X., Sargent, K.E., Lipson, K.L., Hackett, A., Urano, F. Biochem. Biophys. Res. Commun. (2004)
- Spatially regulated ubiquitin ligation by an ER/nuclear membrane ligase. Deng, M., Hochstrasser, M. Nature (2006)
- Human HRD1 protects against ER stress-induced apoptosis through ER-associated degradation. Kaneko, M., Ishiguro, M., Niinuma, Y., Uesugi, M., Nomura, Y. FEBS Lett. (2002)