- Hypersensitivity to N-methyl-N'-nitro-N-nitrosoguanidine in fibroblasts from patients with Huntington disease, familial dysautonomia, and other primary neuronal degenerations. Scudiero, D.A., Meyer, S.A., Clatterbuck, B.E., Tarone, R.E., Robbins, J.H. Proc. Natl. Acad. Sci. U.S.A. (1981)