Chemical Compound Review:
Isoleucine 2-amino-3-methyl-pentanoic acid
Synonyms:
Hile, DL-ISOLEUCINE, DL-ISO-LEUCINE, ISOLEUCINE,(L), AGN-PC-00KEIZ, ...
- On the mechanisms of the formation of L-alloisoleucine and the 2-hydroxy-3-methylvaleric acid stereoisomers from L-isoleucine in maple syrup urine disease patients and in normal humans. Mamer, O.A., Reimer, M.L. J. Biol. Chem. (1992)
- Significance of L-alloisoleucine in plasma for diagnosis of maple syrup urine disease. Schadewaldt, P., Bodner-Leidecker, A., Hammen, H.W., Wendel, U. Clin. Chem. (1999)
- Atypical phenotype in a boy with a maple syrup urine disease. Ben-Omran, T.I., Blaser, S., Phillips, H., Callahan, J., Feigenbaum, A. J. Inherit. Metab. Dis. (2006)
- Leigh disease with deficiency of lipoamide dehydrogenase: treatment failure with dichloroacetate. Craigen, W.J. Pediatric neurology. (1996)
- Isoleucine, an essential amino acid, prevents liver metastases of colon cancer by antiangiogenesis. Murata, K., Moriyama, M. Cancer Res. (2007)
- Oral L-alloisoleucine loading studies in healthy subjects and in patients with maple syrup urine disease. Schadewaldt, P., Dalle-Feste, C., Langenbeck, U., Wendel, U. Pediatr. Res. (1991)
- On the mechanism of L-alloisoleucine formation: studies on a healthy subject and in fibroblasts from normals and patients with maple syrup urine disease. Schadewaldt, P., Hammen, H.W., Dalle-Feste, C., Wendel, U. J. Inherit. Metab. Dis. (1990)
- Branched-chain amino acid interactions in skeletal muscle: isoleucine and L-alloisoleucine. Downey, R.S., Karl, I.E., Bier, D.M. JPEN. Journal of parenteral and enteral nutrition. (1986)
- Alloisoleucine formation in maple syrup urine disease: isotopic evidence for the mechanism. Matthews, D.E., Ben-Galim, E., Haymond, M.W., Bier, D.M. Pediatr. Res. (1980)
- Determination of (S)- and (R)-2-oxo-3-methylvaleric acid in plasma of patients with maple syrup urine disease. Wendel, U., Even, G., Langenbeck, U., Schadewaldt, P., Hummel, W. Clin. Chim. Acta (1992)
- Transamination and oxidative decarboxylation of L-isoleucine, L-alloisoleucine and related 2-oxo acids in perfused rat hind limb muscle. Schadewaldt, P., Radeck, W., Hammen, H.W., Staib, W. Biochim. Biophys. Acta (1989)
- Plasma alloisoleucine: analytical method and clearance in ketoacid-supplemented normals. Ponto, K.H., Anderson, P.A., Kies, C.V. Kidney Int. Suppl. (1989)
- Structural relationships in crystals accommodating different stereoisomers of 2-amino-3-methylpentanoic acid. Dalhus, B., Gorbitz, C.H. Acta Crystallogr., B (2000)